Journal of Multiple Sclerosis and Neuroimmunology 13(2):30-34, 2022
Favorable Response to Rituximab in a Patient with Recurrent Primary Angiitis of the Central Nervous System: A Case Report and Literature Review
Tae Young Kim
Department of Neurology, Gil Medical Center, Gachon University College of Medicine, Incheon, Korea
Primary angiitis of the central nervous system (PACNS) is an uncommon disorder restricted
to the brain and spinal cord and leading to inflammation and destruction of vessels without
evidence of vasculitis outside the central nervous system. Current treatments of PACNS are
based on extrapolation from other forms of systemic vasculitis and retrospective assessments
because there are no prospective studies of therapeutic strategies. We report a case of recurrent
PACNS that showed a successful response to rituximab treatment.
Journal of Multiple Sclerosis and Neuroimmunology 13(2):30-34, 2022
keyword : Central nervous system angiitis; Rituximab; Recurrence
