Primary Central Nervous System Lymphoma Initially Misdiagnosed as Tumefactive Demyelinating Disease
Jiah Kim, MD, Yong-Sung Kim, MD, So-Hyun Park, MD, Il-Han Yoo, MD, Suk-Won Ahn, MD, PhD
Department of Neurology, Chung-Ang University Hospital, Chung-Ang University College of Medicine, Seoul, Korea
Lesions of primary central nervous system lymphoma (PCNSL) are frequently misdiagnosed on brain MRI as tumefactive demyelinating diseases, such as multiple sclerosis (MS) or neuromyelitis optica (NMO). Biopsy may fail to detect tumor cells and indicate only inflammatory cell infiltration with demyelination. Both PCNSL and demyelinating diseases respond to corticosteroid therapy or improve spontaneously. Herein, we describe a patient with a PCNSL who was first diagnosed with tumefactive MS or NMO based on initial brain MRI and biopsy findings.
Journal of Multiple Sclerosis 10(1):18-21, 2019